Complement and inflammasome overactivation mediates paroxysmal nocturnal hemoglobinuria with autoinflammation. [electronic resource]
Producer: 20200622Description: 5123-5136 p. digitalISSN:- 1558-8238
- Aged
- Alleles
- Antibodies, Monoclonal, Humanized -- therapeutic use
- Complement System Proteins -- immunology
- Female
- Gene Deletion
- Genes, X-Linked
- Germany
- Glycosylphosphatidylinositols -- metabolism
- Hemoglobinuria, Paroxysmal -- immunology
- Hemolysis -- drug effects
- Humans
- Inflammasomes -- immunology
- Inflammation -- immunology
- Japan
- Leukocytes -- immunology
- Male
- Membrane Proteins -- genetics
- Middle Aged
- Mutation
- Point Mutation
- THP-1 Cells
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Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't
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