Complement and inflammasome overactivation mediates paroxysmal nocturnal hemoglobinuria with autoinflammation.

Höchsmann, Britta

Complement and inflammasome overactivation mediates paroxysmal nocturnal hemoglobinuria with autoinflammation. [electronic resource] - The Journal of clinical investigation 12 2019 - 5123-5136 p. digital

Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't

1558-8238

10.1172/JCI123501 doi


Aged
Alleles
Antibodies, Monoclonal, Humanized--therapeutic use
Complement System Proteins--immunology
Female
Gene Deletion
Genes, X-Linked
Germany
Glycosylphosphatidylinositols--metabolism
Hemoglobinuria, Paroxysmal--immunology
Hemolysis--drug effects
Humans
Inflammasomes--immunology
Inflammation--immunology
Japan
Leukocytes--immunology
Male
Membrane Proteins--genetics
Middle Aged
Mutation
Point Mutation
THP-1 Cells