Corticosteroid use and increased CXCR2 levels on leukocytes are associated with lumacaftor/ivacaftor discontinuation in cystic fibrosis patients homozygous for the F508del CFTR mutation. [electronic resource]
Producer: 20190514Description: e0209026 p. digitalISSN:- 1932-6203
- Adrenal Cortex Hormones -- therapeutic use
- Adult
- Aminophenols -- adverse effects
- Aminopyridines -- adverse effects
- Benzodioxoles -- adverse effects
- Cystic Fibrosis -- drug therapy
- Cystic Fibrosis Transmembrane Conductance Regulator -- genetics
- Drug Combinations
- Female
- Forced Expiratory Volume
- Gene Deletion
- Homozygote
- Humans
- Leukocytes -- metabolism
- Logistic Models
- Male
- Medication Adherence
- Quinolones -- adverse effects
- Receptors, Interleukin-8B -- metabolism
- Tetraspanin 30 -- metabolism
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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