Corticosteroid use and increased CXCR2 levels on leukocytes are associated with lumacaftor/ivacaftor discontinuation in cystic fibrosis patients homozygous for the F508del CFTR mutation.

Pohl, Kerstin

Corticosteroid use and increased CXCR2 levels on leukocytes are associated with lumacaftor/ivacaftor discontinuation in cystic fibrosis patients homozygous for the F508del CFTR mutation. [electronic resource] - PloS one 2018 - e0209026 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1932-6203

10.1371/journal.pone.0209026 doi


Adrenal Cortex Hormones--therapeutic use
Adult
Aminophenols--adverse effects
Aminopyridines--adverse effects
Benzodioxoles--adverse effects
Cystic Fibrosis--drug therapy
Cystic Fibrosis Transmembrane Conductance Regulator--genetics
Drug Combinations
Female
Forced Expiratory Volume
Gene Deletion
Homozygote
Humans
Leukocytes--metabolism
Logistic Models
Male
Medication Adherence
Quinolones--adverse effects
Receptors, Interleukin-8B--metabolism
Tetraspanin 30--metabolism