Lectin OS-9 delivers mutant neuroserpin to endoplasmic reticulum associated degradation in familial encephalopathy with neuroserpin inclusion bodies. [electronic resource]
Producer: 20150209Description: 2394-403 p. digitalISSN:- 1558-1497
- Animals
- Cells, Cultured
- Disease Models, Animal
- Endoplasmic Reticulum
- Endoplasmic Reticulum-Associated Degradation -- genetics
- Epilepsies, Myoclonic -- genetics
- Glycosylation
- Heredodegenerative Disorders, Nervous System -- genetics
- Humans
- Lectins -- metabolism
- Mice, Transgenic
- Mutation
- Neoplasm Proteins -- metabolism
- Neuropeptides -- genetics
- Polysaccharides -- metabolism
- Proteasome Endopeptidase Complex
- Protein Binding
- Protein Transport
- Proteolysis
- Serpins -- genetics
- Ubiquitin
- Neuroserpin
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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