Lectin OS-9 delivers mutant neuroserpin to endoplasmic reticulum associated degradation in familial encephalopathy with neuroserpin inclusion bodies.

Schipanski, Angela

Lectin OS-9 delivers mutant neuroserpin to endoplasmic reticulum associated degradation in familial encephalopathy with neuroserpin inclusion bodies. [electronic resource] - Neurobiology of aging Oct 2014 - 2394-403 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1558-1497

10.1016/j.neurobiolaging.2014.04.002 doi


Animals
Cells, Cultured
Disease Models, Animal
Endoplasmic Reticulum
Endoplasmic Reticulum-Associated Degradation--genetics
Epilepsies, Myoclonic--genetics
Glycosylation
Heredodegenerative Disorders, Nervous System--genetics
Humans
Lectins--metabolism
Mice, Transgenic
Mutation
Neoplasm Proteins--metabolism
Neuropeptides--genetics
Polysaccharides--metabolism
Proteasome Endopeptidase Complex
Protein Binding
Protein Transport
Proteolysis
Serpins--genetics
Ubiquitin
Neuroserpin