CFTR is involved in the fine tuning of intracellular redox status: physiological implications in cystic fibrosis. [electronic resource]
Producer: 20130206Description: 1367-77 p. digitalISSN:- 1525-2191
- Acetylcysteine -- pharmacology
- Animals
- Carbonic Anhydrases -- metabolism
- Cell Hypoxia -- drug effects
- Cell Line
- Chloride Channels -- metabolism
- Cystic Fibrosis -- metabolism
- Cystic Fibrosis Transmembrane Conductance Regulator -- antagonists & inhibitors
- Disease Models, Animal
- Glutathione -- metabolism
- Green Fluorescent Proteins -- metabolism
- Humans
- Hypoxia-Inducible Factor 1, alpha Subunit -- chemistry
- Intracellular Space -- drug effects
- Kidney Tubules, Proximal -- drug effects
- Male
- Mice
- Mice, Inbred C57BL
- Models, Biological
- Mutation -- genetics
- Osmolar Concentration
- Oxidation-Reduction -- drug effects
- Protein Stability -- drug effects
- Protein Structure, Tertiary
- Reactive Oxygen Species -- metabolism
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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