CFTR is involved in the fine tuning of intracellular redox status: physiological implications in cystic fibrosis.
Duranton, Christophe
CFTR is involved in the fine tuning of intracellular redox status: physiological implications in cystic fibrosis. [electronic resource] - The American journal of pathology Oct 2012 - 1367-77 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1525-2191
10.1016/j.ajpath.2012.06.017 doi
Acetylcysteine--pharmacology
Animals
Carbonic Anhydrases--metabolism
Cell Hypoxia--drug effects
Cell Line
Chloride Channels--metabolism
Cystic Fibrosis--metabolism
Cystic Fibrosis Transmembrane Conductance Regulator--antagonists & inhibitors
Disease Models, Animal
Glutathione--metabolism
Green Fluorescent Proteins--metabolism
Humans
Hypoxia-Inducible Factor 1, alpha Subunit--chemistry
Intracellular Space--drug effects
Kidney Tubules, Proximal--drug effects
Male
Mice
Mice, Inbred C57BL
Models, Biological
Mutation--genetics
Osmolar Concentration
Oxidation-Reduction--drug effects
Protein Stability--drug effects
Protein Structure, Tertiary
Reactive Oxygen Species--metabolism
CFTR is involved in the fine tuning of intracellular redox status: physiological implications in cystic fibrosis. [electronic resource] - The American journal of pathology Oct 2012 - 1367-77 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1525-2191
10.1016/j.ajpath.2012.06.017 doi
Acetylcysteine--pharmacology
Animals
Carbonic Anhydrases--metabolism
Cell Hypoxia--drug effects
Cell Line
Chloride Channels--metabolism
Cystic Fibrosis--metabolism
Cystic Fibrosis Transmembrane Conductance Regulator--antagonists & inhibitors
Disease Models, Animal
Glutathione--metabolism
Green Fluorescent Proteins--metabolism
Humans
Hypoxia-Inducible Factor 1, alpha Subunit--chemistry
Intracellular Space--drug effects
Kidney Tubules, Proximal--drug effects
Male
Mice
Mice, Inbred C57BL
Models, Biological
Mutation--genetics
Osmolar Concentration
Oxidation-Reduction--drug effects
Protein Stability--drug effects
Protein Structure, Tertiary
Reactive Oxygen Species--metabolism