Surfactant protein A2 mutations associated with pulmonary fibrosis lead to protein instability and endoplasmic reticulum stress. [electronic resource]
Producer: 20100806Description: 22103-13 p. digitalISSN:- 1083-351X
- Amino Acid Substitution -- drug effects
- Animals
- Biomarkers -- metabolism
- Bronchoalveolar Lavage Fluid -- chemistry
- Cell Extracts
- Cell Line, Tumor
- Detergents -- pharmacology
- Dogs
- Endoplasmic Reticulum -- drug effects
- Female
- Humans
- Leupeptins -- pharmacology
- Male
- Mutant Proteins -- metabolism
- Mutation -- genetics
- Pedigree
- Protein Processing, Post-Translational -- drug effects
- Protein Stability -- drug effects
- Protein Structure, Quaternary
- Pulmonary Alveoli -- drug effects
- Pulmonary Fibrosis -- genetics
- Pulmonary Surfactant-Associated Protein A -- chemistry
- Solubility -- drug effects
- Stress, Physiological -- drug effects
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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