Alterations in striatal dopamine catabolism precede loss of substantia nigra neurons in a mouse model of juvenile neuronal ceroid lipofuscinosis. [electronic resource]
Producer: 20071019Description: 98-112 p. digitalISSN:- 0006-8993
- Age Factors
- Analysis of Variance
- Animals
- Behavior, Animal -- physiology
- Catechol O-Methyltransferase -- metabolism
- Cell Death -- genetics
- Corpus Striatum -- metabolism
- Disease Models, Animal
- Dopamine -- metabolism
- Gene Expression Regulation -- genetics
- Membrane Glycoproteins -- deficiency
- Mice
- Mice, Knockout
- Models, Biological
- Molecular Chaperones
- Motor Activity -- genetics
- Motor Skills -- physiology
- Neuronal Ceroid-Lipofuscinoses -- genetics
- Neurons -- pathology
- Substantia Nigra -- pathology
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Publication Type: Journal Article; Research Support, N.I.H., Extramural
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