Alterations in striatal dopamine catabolism precede loss of substantia nigra neurons in a mouse model of juvenile neuronal ceroid lipofuscinosis.

Weimer, Jill M

Alterations in striatal dopamine catabolism precede loss of substantia nigra neurons in a mouse model of juvenile neuronal ceroid lipofuscinosis. [electronic resource] - Brain research Aug 2007 - 98-112 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural

0006-8993

10.1016/j.brainres.2007.05.018 doi


Age Factors
Analysis of Variance
Animals
Behavior, Animal--physiology
Catechol O-Methyltransferase--metabolism
Cell Death--genetics
Corpus Striatum--metabolism
Disease Models, Animal
Dopamine--metabolism
Gene Expression Regulation--genetics
Membrane Glycoproteins--deficiency
Mice
Mice, Knockout
Models, Biological
Molecular Chaperones
Motor Activity--genetics
Motor Skills--physiology
Neuronal Ceroid-Lipofuscinoses--genetics
Neurons--pathology
Substantia Nigra--pathology