Methylmalonic acid, a biochemical hallmark of methylmalonic acidurias but no inhibitor of mitochondrial respiratory chain. [electronic resource]
Producer: 20040112Description: 47388-93 p. digitalISSN:- 0021-9258
- Acyl Coenzyme A -- metabolism
- Adenosine Triphosphate -- metabolism
- Aging
- Amino Acid Metabolism, Inborn Errors -- metabolism
- Animals
- Cattle
- Citrates -- metabolism
- Citric Acid Cycle
- Dose-Response Relationship, Drug
- Electron Transport
- Female
- Hydrogen-Ion Concentration
- Male
- Malonates -- metabolism
- Methylmalonic Acid -- chemistry
- Mice
- Mice, Inbred C57BL
- Mitochondria -- metabolism
- Mitochondrial Diseases -- metabolism
- Muscles -- metabolism
- Myocardium -- metabolism
- Oxygen -- metabolism
- Phosphorylation
- Pyruvates -- metabolism
- Spectrophotometry
- Time Factors
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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