Methylmalonic acid, a biochemical hallmark of methylmalonic acidurias but no inhibitor of mitochondrial respiratory chain.

Kölker, Stefan

Methylmalonic acid, a biochemical hallmark of methylmalonic acidurias but no inhibitor of mitochondrial respiratory chain. [electronic resource] - The Journal of biological chemistry Nov 2003 - 47388-93 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0021-9258

10.1074/jbc.M308861200 doi


Acyl Coenzyme A--metabolism
Adenosine Triphosphate--metabolism
Aging
Amino Acid Metabolism, Inborn Errors--metabolism
Animals
Cattle
Citrates--metabolism
Citric Acid Cycle
Dose-Response Relationship, Drug
Electron Transport
Female
Hydrogen-Ion Concentration
Male
Malonates--metabolism
Methylmalonic Acid--chemistry
Mice
Mice, Inbred C57BL
Mitochondria--metabolism
Mitochondrial Diseases--metabolism
Muscles--metabolism
Myocardium--metabolism
Oxygen--metabolism
Phosphorylation
Pyruvates--metabolism
Spectrophotometry
Time Factors