17-AAG increases autophagic removal of mutant androgen receptor in spinal and bulbar muscular atrophy.

Rusmini, Paola

17-AAG increases autophagic removal of mutant androgen receptor in spinal and bulbar muscular atrophy. [electronic resource] - Neurobiology of disease Jan 2011 - 83-95 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1095-953X

10.1016/j.nbd.2010.08.023 doi


Animals
Autophagy--drug effects
Benzoquinones--pharmacology
Cell Line, Transformed
Lactams, Macrocyclic--pharmacology
Mice
Motor Neurons--drug effects
Muscular Atrophy, Spinal--drug therapy
Mutation--genetics
Neuroprotective Agents--pharmacology
Proteostasis Deficiencies--drug therapy
Receptors, Androgen--genetics
Up-Regulation--drug effects