Restoration of copper metabolism and rescue of hepatic abnormalities in LEC rats, an animal model of Wilson disease, by expression of human ATP7B gene.
Meng, Yan
Restoration of copper metabolism and rescue of hepatic abnormalities in LEC rats, an animal model of Wilson disease, by expression of human ATP7B gene. [electronic resource] - Biochimica et biophysica acta Nov 2004 - 208-19 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
0006-3002
10.1016/j.bbadis.2004.06.022 doi
Adenosine Triphosphatases--genetics
Aging--physiology
Animals
Animals, Genetically Modified
Carcinoma, Hepatocellular--genetics
Cation Transport Proteins--genetics
Ceruloplasmin--biosynthesis
Copper--metabolism
Copper-Transporting ATPases
Disease Models, Animal
Female
Gene Expression
Hepatitis, Animal--genetics
Hepatolenticular Degeneration--genetics
Humans
Iron--metabolism
Liver--abnormalities
Rats
Rats, Inbred LEC
Rats, Sprague-Dawley
Survival Rate
Transgenes--genetics
Restoration of copper metabolism and rescue of hepatic abnormalities in LEC rats, an animal model of Wilson disease, by expression of human ATP7B gene. [electronic resource] - Biochimica et biophysica acta Nov 2004 - 208-19 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
0006-3002
10.1016/j.bbadis.2004.06.022 doi
Adenosine Triphosphatases--genetics
Aging--physiology
Animals
Animals, Genetically Modified
Carcinoma, Hepatocellular--genetics
Cation Transport Proteins--genetics
Ceruloplasmin--biosynthesis
Copper--metabolism
Copper-Transporting ATPases
Disease Models, Animal
Female
Gene Expression
Hepatitis, Animal--genetics
Hepatolenticular Degeneration--genetics
Humans
Iron--metabolism
Liver--abnormalities
Rats
Rats, Inbred LEC
Rats, Sprague-Dawley
Survival Rate
Transgenes--genetics