000 01287 a2200397 4500
005 20250512072222.0
264 0 _c19870105
008 198701s 0 0 eng d
022 _a0031-4005
040 _aNLM
_beng
_cNLM
100 1 _aDuran, M
245 0 0 _aSudden child death and 'healthy' affected family members with medium-chain acyl-coenzyme A dehydrogenase deficiency.
_h[electronic resource]
260 _bPediatrics
_cDec 1986
300 _a1052-7 p.
_bdigital
500 _aPublication Type: Case Reports; Journal Article
650 0 4 _aAcyl-CoA Dehydrogenase
650 0 4 _aCaproates
_xmetabolism
650 0 4 _aCaprylates
_xmetabolism
650 0 4 _aDecanoic Acids
_xmetabolism
650 0 4 _aFatty Acid Desaturases
_xanalysis
650 0 4 _aFatty Acids
_xmetabolism
650 0 4 _aFatty Acids, Nonesterified
_xmetabolism
650 0 4 _aFemale
650 0 4 _aHumans
650 0 4 _aInfant
650 0 4 _aLipid Metabolism, Inborn Errors
_xenzymology
650 0 4 _aMale
650 0 4 _aMitochondria, Liver
_xanalysis
650 0 4 _aOxidation-Reduction
650 0 4 _aSudden Infant Death
_xetiology
700 1 _aHofkamp, M
700 1 _aRhead, W J
700 1 _aSaudubray, J M
700 1 _aWadman, S K
773 0 _tPediatrics
_gvol. 78
_gno. 6
_gp. 1052-7
999 _c3791724
_d3791724