000 01795 a2200505 4500
005 20250518095812.0
264 0 _c20210104
008 202101s 0 0 eng d
022 _a1879-260X
024 7 _a10.1016/j.bbadis.2020.165800
_2doi
040 _aNLM
_beng
_cNLM
100 1 _aFernández, Gabriela
245 0 0 _aMyofibers deficient in connexins 43 and 45 expression protect mice from skeletal muscle and systemic dysfunction promoted by a dysferlin mutation.
_h[electronic resource]
260 _bBiochimica et biophysica acta. Molecular basis of disease
_c08 2020
300 _a165800 p.
_bdigital
500 _aPublication Type: Journal Article; Research Support, Non-U.S. Gov't
650 0 4 _aAnimals
650 0 4 _aCalcium
_xmetabolism
650 0 4 _aConnexin 43
_xdeficiency
650 0 4 _aConnexins
_xdeficiency
650 0 4 _aCreatine Kinase
_xblood
650 0 4 _aDisease Models, Animal
650 0 4 _aDysferlin
_xdeficiency
650 0 4 _aGene Expression
650 0 4 _aHumans
650 0 4 _aMale
650 0 4 _aMice
650 0 4 _aMice, Inbred C57BL
650 0 4 _aMice, Knockout
650 0 4 _aMuscular Dystrophies, Limb-Girdle
_xgenetics
650 0 4 _aMutation
650 0 4 _aMyofibrils
_xgenetics
650 0 4 _aPermeability
650 0 4 _aPhysical Conditioning, Animal
650 0 4 _aRotarod Performance Test
650 0 4 _aSarcolemma
_xmetabolism
700 1 _aArias-Bravo, Guisselle
700 1 _aBevilacqua, Jorge A
700 1 _aCastillo-Ruiz, Mario
700 1 _aCaviedes, Pablo
700 1 _aSáez, Juan C
700 1 _aCea, Luis A
773 0 _tBiochimica et biophysica acta. Molecular basis of disease
_gvol. 1866
_gno. 8
_gp. 165800
856 4 0 _uhttps://doi.org/10.1016/j.bbadis.2020.165800
_zAvailable from publisher's website
999 _c30872255
_d30872255