000 01705 a2200433 4500
005 20250517121619.0
264 0 _c20180104
008 201801s 0 0 eng d
022 _a1873-5010
024 7 _a10.1016/j.jcf.2016.09.003
_2doi
040 _aNLM
_beng
_cNLM
100 1 _aSermet-Gaudelus, Isabelle
245 0 0 _aBone demineralization is improved by ivacaftor in patients with cystic fibrosis carrying the p.Gly551Asp mutation.
_h[electronic resource]
260 _bJournal of cystic fibrosis : official journal of the European Cystic Fibrosis Society
_c11 2016
300 _ae67-e69 p.
_bdigital
500 _aPublication Type: Journal Article; Research Support, Non-U.S. Gov't
650 0 4 _aAdult
650 0 4 _aAminophenols
_xadministration & dosage
650 0 4 _aBone Demineralization, Pathologic
_xetiology
650 0 4 _aBone Density
_xdrug effects
650 0 4 _aCells, Cultured
650 0 4 _aChloride Channel Agonists
_xadministration & dosage
650 0 4 _aCystic Fibrosis
_xcomplications
650 0 4 _aCystic Fibrosis Transmembrane Conductance Regulator
_xgenetics
650 0 4 _aFemale
650 0 4 _aHumans
650 0 4 _aMale
650 0 4 _aMiddle Aged
650 0 4 _aMutation
650 0 4 _aOsteoblasts
_xdrug effects
650 0 4 _aQuinolones
_xadministration & dosage
650 0 4 _aStatistics as Topic
700 1 _aDelion, Martial
700 1 _aDurieu, Isabelle
700 1 _aJacquot, Jacky
700 1 _aHubert, Dominique
773 0 _tJournal of cystic fibrosis : official journal of the European Cystic Fibrosis Society
_gvol. 15
_gno. 6
_gp. e67-e69
856 4 0 _uhttps://doi.org/10.1016/j.jcf.2016.09.003
_zAvailable from publisher's website
999 _c26519540
_d26519540