000 | 02386 a2200577 4500 | ||
---|---|---|---|
005 | 20250517001046.0 | ||
264 | 0 | _c20150311 | |
008 | 201503s 0 0 eng d | ||
022 | _a1522-1504 | ||
024 | 7 |
_a10.1152/ajplung.00217.2014 _2doi |
|
040 |
_aNLM _beng _cNLM |
||
100 | 1 | _aHawkins, Arie | |
245 | 0 | 0 |
_aA non-BRICHOS SFTPC mutant (SP-CI73T) linked to interstitial lung disease promotes a late block in macroautophagy disrupting cellular proteostasis and mitophagy. _h[electronic resource] |
260 |
_bAmerican journal of physiology. Lung cellular and molecular physiology _cJan 2015 |
||
300 |
_aL33-47 p. _bdigital |
||
500 | _aPublication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, Non-P.H.S. | ||
650 | 0 | 4 |
_aATP-Binding Cassette Transporters _xgenetics |
650 | 0 | 4 |
_aAdaptor Proteins, Signal Transducing _xbiosynthesis |
650 | 0 | 4 | _aAmino Acid Substitution |
650 | 0 | 4 | _aAutophagy |
650 | 0 | 4 | _aAutophagy-Related Protein 8 Family |
650 | 0 | 4 | _aFemale |
650 | 0 | 4 |
_aGene Expression Regulation _xgenetics |
650 | 0 | 4 |
_aGenetic Diseases, Inborn _xgenetics |
650 | 0 | 4 | _aHEK293 Cells |
650 | 0 | 4 | _aHumans |
650 | 0 | 4 | _aInfant |
650 | 0 | 4 |
_aLung Diseases, Interstitial _xgenetics |
650 | 0 | 4 |
_aLysosomes _xgenetics |
650 | 0 | 4 |
_aMembrane Potential, Mitochondrial _xgenetics |
650 | 0 | 4 |
_aMicrofilament Proteins _xbiosynthesis |
650 | 0 | 4 |
_aMicrotubule-Associated Proteins _xbiosynthesis |
650 | 0 | 4 |
_aMitochondria _xgenetics |
650 | 0 | 4 | _aMutation, Missense |
650 | 0 | 4 |
_aProteostasis Deficiencies _xgenetics |
650 | 0 | 4 |
_aPulmonary Surfactant-Associated Protein C _xgenetics |
650 | 0 | 4 | _aSequestosome-1 Protein |
650 | 0 | 4 |
_aUbiquitin-Protein Ligases _xbiosynthesis |
650 | 0 | 4 |
_aVacuoles _xgenetics |
650 | 0 | 4 |
_arab GTP-Binding Proteins _xbiosynthesis |
650 | 0 | 4 | _arab7 GTP-Binding Proteins |
700 | 1 | _aGuttentag, Susan H | |
700 | 1 | _aDeterding, Robin | |
700 | 1 | _aFunkhouser, William K | |
700 | 1 | _aGoralski, Jennifer L | |
700 | 1 | _aChatterjee, Shampa | |
700 | 1 | _aMulugeta, Surafel | |
700 | 1 | _aBeers, Michael F | |
773 | 0 |
_tAmerican journal of physiology. Lung cellular and molecular physiology _gvol. 308 _gno. 1 _gp. L33-47 |
|
856 | 4 | 0 |
_uhttps://doi.org/10.1152/ajplung.00217.2014 _zAvailable from publisher's website |
999 |
_c24304852 _d24304852 |