000 01680 a2200493 4500
005 20250516213621.0
264 0 _c20150603
008 201506s 0 0 eng d
022 _a1460-2083
024 7 _a10.1093/hmg/ddu254
_2doi
040 _aNLM
_beng
_cNLM
100 1 _aZulian, Alessandra
245 0 0 _aNIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models.
_h[electronic resource]
260 _bHuman molecular genetics
_cOct 2014
300 _a5353-63 p.
_bdigital
500 _aPublication Type: Journal Article; Research Support, Non-U.S. Gov't
650 0 4 _aAnimals
650 0 4 _aApoptosis
_xdrug effects
650 0 4 _aCells, Cultured
650 0 4 _aCollagen Type VI
_xgenetics
650 0 4 _aCyclosporine
_xadministration & dosage
650 0 4 _aDisease Models, Animal
650 0 4 _aHumans
650 0 4 _aMice
650 0 4 _aMitochondria
_xmetabolism
650 0 4 _aMuscle Strength
_xdrug effects
650 0 4 _aMuscular Dystrophies
_xcongenital
650 0 4 _aZebrafish
650 0 4 _aZebrafish Proteins
_xgenetics
700 1 _aRizzo, Erika
700 1 _aSchiavone, Marco
700 1 _aPalma, Elena
700 1 _aTagliavini, Francesca
700 1 _aBlaauw, Bert
700 1 _aMerlini, Luciano
700 1 _aMaraldi, Nadir Mario
700 1 _aSabatelli, Patrizia
700 1 _aBraghetta, Paola
700 1 _aBonaldo, Paolo
700 1 _aArgenton, Francesco
700 1 _aBernardi, Paolo
773 0 _tHuman molecular genetics
_gvol. 23
_gno. 20
_gp. 5353-63
856 4 0 _uhttps://doi.org/10.1093/hmg/ddu254
_zAvailable from publisher's website
999 _c23848041
_d23848041