000 01762 a2200517 4500
005 20250513214153.0
264 0 _c20000915
008 200009s 0 0 eng d
022 _a0960-8966
024 7 _a10.1016/s0960-8966(00)00108-5
_2doi
040 _aNLM
_beng
_cNLM
100 1 _aVorgerd, M
245 0 0 _aMitochondrial impairment of human muscle in Friedreich ataxia in vivo.
_h[electronic resource]
260 _bNeuromuscular disorders : NMD
_cAug 2000
300 _a430-5 p.
_bdigital
500 _aPublication Type: Clinical Trial; Controlled Clinical Trial; Journal Article; Research Support, Non-U.S. Gov't
650 0 4 _aAdenosine Triphosphate
_xbiosynthesis
650 0 4 _aAdolescent
650 0 4 _aAdult
650 0 4 _aAge Factors
650 0 4 _aAlleles
650 0 4 _aExercise Test
650 0 4 _aFemale
650 0 4 _aFriedreich Ataxia
_xgenetics
650 0 4 _aHumans
650 0 4 _aIron-Binding Proteins
650 0 4 _aIsometric Contraction
650 0 4 _aMagnetic Resonance Spectroscopy
650 0 4 _aMale
650 0 4 _aMiddle Aged
650 0 4 _aMitochondria, Muscle
_xmetabolism
650 0 4 _aMuscle, Skeletal
_xmetabolism
650 0 4 _aMuscular Dystrophy, Duchenne
_xmetabolism
650 0 4 _aPhosphocreatine
_xmetabolism
650 0 4 _aPhosphorus Isotopes
_xanalysis
650 0 4 _aPhosphotransferases (Alcohol Group Acceptor)
_xgenetics
650 0 4 _aTrinucleotide Repeats
_xgenetics
650 0 4 _aFrataxin
700 1 _aSchöls, L
700 1 _aHardt, C
700 1 _aRistow, M
700 1 _aEpplen, J T
700 1 _aZange, J
773 0 _tNeuromuscular disorders : NMD
_gvol. 10
_gno. 6
_gp. 430-5
856 4 0 _uhttps://doi.org/10.1016/s0960-8966(00)00108-5
_zAvailable from publisher's website
999 _c10849822
_d10849822