Increased solubility of lamins and redistribution of lamin C in X-linked Emery-Dreifuss muscular dystrophy fibroblasts. [electronic resource]
Producer: 20030627Description: 241-53 p. digitalISSN:- 1047-8477
- Cell Nucleus -- metabolism
- Cell Separation
- Chromosomes, Human, X
- DNA-Binding Proteins -- metabolism
- Deoxyribonuclease I -- metabolism
- Dose-Response Relationship, Drug
- Fibroblasts -- metabolism
- Flow Cytometry
- Fluorescent Antibody Technique, Indirect
- Humans
- Immunoblotting
- Lamin Type A -- metabolism
- Lamins -- metabolism
- Membrane Proteins -- metabolism
- Microscopy, Confocal
- Microscopy, Fluorescence
- Muscular Dystrophy, Emery-Dreifuss -- metabolism
- Mutation
- Nuclear Envelope -- metabolism
- Nuclear Lamina -- metabolism
- Ribonuclease, Pancreatic -- metabolism
- Skin -- metabolism
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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