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	1.	Bile acid analysis in human disorders of bile acid biosynthesis. [electronic resource] by Vaz, Frédéric M Ferdinandusse, Sacha Producer: 20180409 In: Molecular aspects of medicine vol. 56 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	2.	Carnitine biosynthesis in mammals. [electronic resource] by Vaz, Frédéric M Wanders, Ronald J A Producer: 20020312 In: The Biochemical journal vol. 361 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	3.	Enzymology of the carnitine biosynthesis pathway. [electronic resource] by Strijbis, Karin Vaz, Frédéric M Distel, Ben Producer: 20100713 In: IUBMB life vol. 62 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	4.	Dietary fat and fiber interactively modulate apoptosis and mitochondrial bioenergetic profiles in mouse colon in a site-specific manner. [electronic resource] by Fan, Yang-Yi Vaz, Frederic M Chapkin, Robert S Producer: 20180326 In: European journal of cancer prevention : the official journal of the European Cancer Prevention Organisation (ECP) vol. 26 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	5.	Extended Abstract: Deficiency of Sodium Taurocholate Cotransporting Polypeptide (SLC10A1): A New Inborn Error of Metabolism with an Attenuated Phenotype. [electronic resource] by Vaz, Frédéric M Huidekoper, Hidde H Paulusma, Coen C Producer: 20170501 In: Digestive diseases (Basel, Switzerland) vol. 35 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	6.	Measurement of carnitine biosynthesis enzyme activities by tandem mass spectrometry: differences between the mouse and the rat. [electronic resource] by van Vlies, Naomi Wanders, Ronald J A Vaz, Frédéric M Producer: 20061012 In: Analytical biochemistry vol. 354 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	7.	Hepatotoxicity due to chenodeoxycholic acid supplementation in an infant with cerebrotendinous xanthomatosis: implications for treatment. [electronic resource] by Huidekoper, Hidde H Vaz, Frédéric M Verrips, Aad Bosch, Annet M Producer: 20161108 In: European journal of pediatrics vol. 175 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	8.	Submitochondrial localization of 6-N-trimethyllysine dioxygenase - implications for carnitine biosynthesis. [electronic resource] by van Vlies, Naomi Ofman, Rob Wanders, Ronald J A Vaz, Frédéric M Producer: 20080129 In: The FEBS journal vol. 274 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	9.	Acylcarnitines: reflecting or inflicting insulin resistance? [electronic resource] by Schooneman, Marieke G Vaz, Frédéric M Houten, Sander M Soeters, Maarten R Producer: 20130308 In: Diabetes vol. 62 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	10.	Meijer and Vloedman's histochemical demonstration of mitochondrial coupling obeys Lambert-Beer's law in the myocardium. [electronic resource] by Peters, Eva L Comerford, David Vaz, Frédéric M van der Laarse, Willem J Producer: 20190118 In: Histochemistry and cell biology vol. 151 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	11.	The human TAZ gene complements mitochondrial dysfunction in the yeast taz1Delta mutant. Implications for Barth syndrome. [electronic resource] by Ma, Lining Vaz, Frederic M Gu, Zhiming Wanders, Ronald J A Greenberg, Miriam L Producer: 20041214 In: The Journal of biological chemistry vol. 279 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	12.	Principles and practice of lipidomics. [electronic resource] by Vaz, Frédéric M Pras-Raves, Mia Bootsma, Albert H van Kampen, Antoine H C Producer: 20151008 In: Journal of inherited metabolic disease vol. 38 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	13.	Slc22a5 haploinsufficiency does not aggravate the phenotype of the long-chain acyl-CoA dehydrogenase KO mouse. [electronic resource] by Ranea-Robles, Pablo Yu, Chunli van Vlies, Naomi Vaz, Frédéric M Houten, Sander M Producer: 20210823 In: Journal of inherited metabolic disease vol. 43 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	14.	PPAR alpha-activation results in enhanced carnitine biosynthesis and OCTN2-mediated hepatic carnitine accumulation. [electronic resource] by van Vlies, Naomi Ferdinandusse, Sacha Turkenburg, Marjolein Wanders, Ronald J A Vaz, Frédéric M Producer: 20071015 In: Biochimica et biophysica acta vol. 1767 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	15.	The important role of biochemical and functional studies in the diagnostics of peroxisomal disorders. [electronic resource] by Ferdinandusse, Sacha Ebberink, Merel S Vaz, Frédéric M Waterham, Hans R Wanders, Ronald J A Producer: 20171204 In: Journal of inherited metabolic disease vol. 39 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	16.	Only one splice variant of the human TAZ gene encodes a functional protein with a role in cardiolipin metabolism. [electronic resource] by Vaz, Frédéric M Houtkooper, Riekelt H Valianpour, Fredoen Barth, Peter G Wanders, Ronald J A Producer: 20031224 In: The Journal of biological chemistry vol. 278 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	17.	Delineating the role of alterations in lipid metabolism to the pathogenesis of inherited skeletal and cardiac muscle disorders: Thematic Review Series: Genetics of Human Lipid Diseases. [electronic resource] by Saini-Chohan, Harjot K Mitchell, Ryan W Vaz, Frédéric M Zelinski, Teresa Hatch, Grant M Producer: 20120409 In: Journal of lipid research vol. 53 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	18.	An improved enzyme assay for carnitine palmitoyl transferase I in fibroblasts using tandem mass spectrometry. [electronic resource] by van Vlies, Naomi Ruiter, Jos P N Doolaard, Mirjam Wanders, Ronald J A Vaz, Frédéric M Producer: 20071206 In: Molecular genetics and metabolism vol. 90 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	19.	Update on newborn dried bloodspot testing for cerebrotendinous xanthomatosis: An available high-throughput liquid-chromatography tandem mass spectrometry method. [electronic resource] by Bleyle, Lisa Huidekoper, Hidde H Vaz, Frederic M Singh, Renu Steiner, Robert D DeBarber, Andrea E Producer: 20160622 In: Molecular genetics and metabolism reports vol. 7 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	20.	Carnitine biosynthesis in Neurospora crassa: identification of a cDNA coding for epsilon-N-trimethyllysine hydroxylase and its functional expression in Saccharomyces cerevisiae. [electronic resource] by Swiegers, Jan H Vaz, Frédéric M Pretorius, Isak S Wanders, Ronald J A Bauer, Florian F Producer: 20020722 In: FEMS microbiology letters vol. 210 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)

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Your search returned 103 results.