Mutant huntingtin disrupts mitochondrial proteostasis by interacting with TIM23. [electronic resource]
Producer: 20200325Description: 16593-16602 p. digitalISSN:- 1091-6490
- Cell Line
- Cell Nucleus -- metabolism
- Cerebral Cortex -- pathology
- Corpus Striatum -- pathology
- Humans
- Huntingtin Protein -- metabolism
- Huntington Disease
- Mitochondria -- metabolism
- Mitochondrial Membrane Transport Proteins -- metabolism
- Mitochondrial Membranes -- metabolism
- Mitochondrial Precursor Protein Import Complex Proteins
- Mitochondrial Proteins -- metabolism
- Mutant Proteins -- metabolism
- Protein Binding
- Proteome -- metabolism
- Proteostasis
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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