Enhanced autophagy and mitochondrial aberrations in murine G(M1)-gangliosidosis. [electronic resource]
Producer: 20080304Description: 616-22 p. digitalISSN:- 1090-2104
- Adenine -- analogs & derivatives
- Adenosine Triphosphate -- pharmacology
- Animals
- Apoptosis Regulatory Proteins
- Astrocytes -- drug effects
- Autophagy -- drug effects
- Beclin-1
- Brain -- pathology
- Cells, Cultured
- Disease Models, Animal
- Electron Transport Complex IV -- metabolism
- Enzyme Inhibitors -- pharmacology
- G(M1) Ganglioside -- metabolism
- Gangliosidosis, GM1 -- genetics
- Lysosomes -- metabolism
- Mice
- Mice, Knockout
- Microtubule-Associated Proteins -- metabolism
- Mitochondria -- enzymology
- Paraquat -- pharmacology
- Protein Kinases -- metabolism
- Proteins -- metabolism
- Signal Transduction -- genetics
- TOR Serine-Threonine Kinases
- beta-Galactosidase -- deficiency
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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