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	1.	Genistein increases glycosaminoglycan levels in mucopolysaccharidosis type I cell models. [electronic resource] by Kingma, Sandra D K Wagemans, Tom IJlst, Lodewijk Wijburg, Frits A van Vlies, Naomi Producer: 20150515 In: Journal of inherited metabolic disease vol. 37 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	2.	Direct nonisotopic assay of 3-methylglutaconyl-CoA hydratase in cultured human skin fibroblasts to specifically identify patients with 3-methylglutaconic aciduria type I. [electronic resource] by Loupatty, Ference J Ruiter, Jos P N IJlst, Lodewijk Duran, Marinus Wanders, Ronald J A Producer: 20040823 In: Clinical chemistry vol. 50 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	3.	A role for the human peroxisomal half-transporter ABCD3 in the oxidation of dicarboxylic acids. [electronic resource] by van Roermund, Carlo W T Ijlst, Lodewijk Wagemans, Tom Wanders, Ronald J A Waterham, Hans R Producer: 20140528 In: Biochimica et biophysica acta vol. 1841 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	4.	The enzymology of mitochondrial fatty acid beta-oxidation and its application to follow-up analysis of positive neonatal screening results. [electronic resource] by Wanders, Ronald J A Ruiter, Jos P N IJLst, Lodewijk Waterham, Hans R Houten, Sander M Producer: 20110128 In: Journal of inherited metabolic disease vol. 33 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	5.	dif-1 and colt, both implicated in early embryonic development, encode carnitine acylcarnitine translocase. [electronic resource] by Oey, Nadia A Ijlst, Lodewijk van Roermund, Carlo W T Wijburg, Frits A Wanders, Ronald J A Producer: 20051025 In: Molecular genetics and metabolism vol. 85 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	6.	Metabolite transport across the peroxisomal membrane. [electronic resource] by Visser, Wouter F van Roermund, Carlo W T Ijlst, Lodewijk Waterham, Hans R Wanders, Ronald J A Producer: 20070116 In: The Biochemical journal vol. 401 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	7.	Carnitine palmitoyltransferase 2: New insights on the substrate specificity and implications for acylcarnitine profiling. [electronic resource] by Violante, Sara Ijlst, Lodewijk van Lenthe, Henk de Almeida, Isabel Tavares Wanders, Ronald J Ventura, Fátima V Producer: 20101116 In: Biochimica et biophysica acta vol. 1802 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	8.	Demonstration of bile acid transport across the mammalian peroxisomal membrane. [electronic resource] by Visser, Wouter F van Roermund, Carlo W T Ijlst, Lodewijk Waterham, Hans R Wanders, Ronald J A Producer: 20070605 In: Biochemical and biophysical research communications vol. 357 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	9.	The Brown-Vialetto-Van Laere and Fazio Londe syndrome revisited: natural history, genetics, treatment and future perspectives. [electronic resource] by Bosch, Annet M Stroek, Kevin Abeling, Nico G Waterham, Hans R Ijlst, Lodewijk Wanders, Ronald J A Producer: 20130410 In: Orphanet journal of rare diseases vol. 7 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	10.	Differential substrate specificities of human ABCD1 and ABCD2 in peroxisomal fatty acid β-oxidation. [electronic resource] by van Roermund, Carlo W T Visser, Wouter F Ijlst, Lodewijk Waterham, Hans R Wanders, Ronald J A Producer: 20110329 In: Biochimica et biophysica acta vol. 1811 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	11.	3-Methylglutaconic aciduria type I is caused by mutations in AUH. [electronic resource] by IJlst, Lodewijk Loupatty, Ference J Ruiter, Jos P N Duran, Marinus Lehnert, Willy Wanders, Ronald J A Producer: 20030123 In: American journal of human genetics vol. 71 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	12.	Arginine improves peroxisome functioning in cells from patients with a mild peroxisome biogenesis disorder. [electronic resource] by Berendse, Kevin Ebberink, Merel S Ijlst, Lodewijk Poll-The, Bwee Tien Wanders, Ronald J A Waterham, Hans R Producer: 20140717 In: Orphanet journal of rare diseases vol. 8 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	13.	Demonstration and characterization of phosphate transport in mammalian peroxisomes. [electronic resource] by Visser, Wouter F Van Roermund, Carlo W Ijlst, Lodewijk Hellingwerf, Klaas J Wanders, Ronald J A Waterham, Hans R Producer: 20051104 In: The Biochemical journal vol. 389 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	14.	Fatty acid oxidation in the human fetus: implications for fetal and adult disease. [electronic resource] by Oey, Nadia A Ruiter, Jos P N Attié-Bitach, Tania Ijlst, Lodewijk Wanders, Ronald J A Wijburg, Frits A Producer: 20061016 In: Journal of inherited metabolic disease vol. 29 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	15.	Characterization of L-aminocarnitine, an inhibitor of fatty acid oxidation. [electronic resource] by Chegary, Malika Te Brinke, Heleen Doolaard, Mirjam Ijlst, Lodewijk Wijburg, Frits A Wanders, Ronald J A Houten, Sander M Producer: 20080421 In: Molecular genetics and metabolism vol. 93 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	16.	Prediction of phenotypic severity in mucopolysaccharidosis type IIIA. [electronic resource] by Knottnerus, Suzan J G Nijmeijer, Stephanie C M IJlst, Lodewijk Te Brinke, Heleen van Vlies, Naomi Wijburg, Frits A Producer: 20171222 In: Annals of neurology vol. 82 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	17.	Valproyl-dephosphoCoA: a novel metabolite of valproate formed in vitro in rat liver mitochondria. [electronic resource] by Silva, Margarida F B Ijlst, Lodewijk Allers, Paul Jakobs, Cornelis Duran, Marinus de Almeida, Isabel Tavares Wanders, Ronald J A Producer: 20050201 In: Drug metabolism and disposition: the biological fate of chemicals vol. 32 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	18.	First identification of a 2-ketoglutarate/isocitrate transport system in mammalian peroxisomes and its characterization. [electronic resource] by Visser, Wouter F van Roermund, Carlo W T Ijlst, Lodewijk Hellingwerf, Klaas J Waterham, Hans R Wanders, Ronald J A Producer: 20061019 In: Biochemical and biophysical research communications vol. 348 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	19.	Identification of the human mitochondrial FAD transporter and its potential role in multiple acyl-CoA dehydrogenase deficiency. [electronic resource] by Spaan, András N Ijlst, Lodewijk van Roermund, Carlo W T Wijburg, Frits A Wanders, Ronald J A Waterham, Hans R Producer: 20060227 In: Molecular genetics and metabolism vol. 86 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	20.	Adverse Effects of Genistein in a Mucopolysaccharidosis Type I Mouse Model. [electronic resource] by Kingma, Sandra D K Wagemans, Tom IJlst, Lodewijk Seppen, Jurgen Gijbels, Marion J J Wijburg, Frits A van Vlies, Naomi Producer: 20150630 In: JIMD reports vol. 23 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)

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Your search returned 58 results.