Extracellular matrix disruption is an early event in the pathogenesis of skeletal disease in mucopolysaccharidosis I. [electronic resource]
Producer: 20151028Description: 146-55 p. digitalISSN:- 1096-7206
- Animals
- Biglycan -- metabolism
- Bone Diseases -- etiology
- Collagen Type I -- metabolism
- Disease Models, Animal
- Extracellular Matrix -- metabolism
- Extracellular Matrix Proteins -- metabolism
- Eye Proteins -- metabolism
- Fibromodulin
- Gene Expression Profiling
- Glycoproteins -- metabolism
- Glycosaminoglycans -- metabolism
- Immunohistochemistry
- Lactoferrin -- metabolism
- Mass Spectrometry
- Mice
- Mice, Knockout
- Mucopolysaccharidosis I -- metabolism
- Nerve Growth Factors -- metabolism
- Osteoarthritis -- etiology
- Proteoglycans -- metabolism
- Proteomics
- Serpins -- metabolism
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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