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A mutation in MT-TW causes a tRNA processing defect and reduced mitochondrial function in a family with Leigh syndrome. [electronic resource] by
- Duff, Rachael M
- Shearwood, Anne-Marie J
- Ermer, Judith
- Rossetti, Giulia
- Gooding, Rebecca
- Richman, Tara R
- Balasubramaniam, Shanti
- Thorburn, David R
- Rackham, Oliver
- Lamont, Phillipa J
- Filipovska, Aleksandra
Producer: 20160825
In:
Mitochondrion vol. 25
Availability: No items available.
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Concerted regulation of mitochondrial and nuclear non-coding RNAs by a dual-targeted RNase Z. [electronic resource] by
- Siira, Stefan J
- Rossetti, Giulia
- Richman, Tara R
- Perks, Kara
- Ermer, Judith A
- Kuznetsova, Irina
- Hughes, Laetitia
- Shearwood, Anne-Marie J
- Viola, Helena M
- Hool, Livia C
- Rackham, Oliver
- Filipovska, Aleksandra
Producer: 20190606
In:
EMBO reports vol. 19
Availability: No items available.
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Loss of the RNA-binding protein TACO1 causes late-onset mitochondrial dysfunction in mice. [electronic resource] by
- Richman, Tara R
- Spåhr, Henrik
- Ermer, Judith A
- Davies, Stefan M K
- Viola, Helena M
- Bates, Kristyn A
- Papadimitriou, John
- Hool, Livia C
- Rodger, Jennifer
- Larsson, Nils-Göran
- Rackham, Oliver
- Filipovska, Aleksandra
Producer: 20180822
In:
Nature communications vol. 7
Availability: No items available.
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Murine cytomegalovirus infection exacerbates complex IV deficiency in a model of mitochondrial disease. [electronic resource] by
- Ferreira, Nicola
- Andoniou, Christopher E
- Perks, Kara L
- Ermer, Judith A
- Rudler, Danielle L
- Rossetti, Giulia
- Periyakaruppiah, Ambika
- Wong, Jamie K Y
- Rackham, Oliver
- Noakes, Peter G
- Degli-Esposti, Mariapia A
- Filipovska, Aleksandra
Producer: 20200615
In:
PLoS genetics vol. 16
Availability: No items available.
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Adult-onset obesity is triggered by impaired mitochondrial gene expression. [electronic resource] by
- Perks, Kara L
- Ferreira, Nicola
- Richman, Tara R
- Ermer, Judith A
- Kuznetsova, Irina
- Shearwood, Anne-Marie J
- Lee, Richard G
- Viola, Helena M
- Johnstone, Victoria P A
- Matthews, Vance
- Hool, Livia C
- Rackham, Oliver
- Filipovska, Aleksandra
Producer: 20190628
In:
Science advances vol. 3
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Hierarchical RNA Processing Is Required for Mitochondrial Ribosome Assembly. [electronic resource] by
- Rackham, Oliver
- Busch, Jakob D
- Matic, Stanka
- Siira, Stefan J
- Kuznetsova, Irina
- Atanassov, Ilian
- Ermer, Judith A
- Shearwood, Anne-Marie J
- Richman, Tara R
- Stewart, James B
- Mourier, Arnaud
- Milenkovic, Dusanka
- Larsson, Nils-Göran
- Filipovska, Aleksandra
Producer: 20171113
In:
Cell reports vol. 16
Availability: No items available.
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10.
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Fidelity of translation initiation is required for coordinated respiratory complex assembly. [electronic resource] by
- Rudler, Danielle L
- Hughes, Laetitia A
- Perks, Kara L
- Richman, Tara R
- Kuznetsova, Irina
- Ermer, Judith A
- Abudulai, Laila N
- Shearwood, Anne-Marie J
- Viola, Helena M
- Hool, Livia C
- Siira, Stefan J
- Rackham, Oliver
- Filipovska, Aleksandra
Producer: 20200721
In:
Science advances vol. 5
Availability: No items available.
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11.
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PTCD1 Is Required for 16S rRNA Maturation Complex Stability and Mitochondrial Ribosome Assembly. [electronic resource] by
- Perks, Kara L
- Rossetti, Giulia
- Kuznetsova, Irina
- Hughes, Laetitia A
- Ermer, Judith A
- Ferreira, Nicola
- Busch, Jakob D
- Rudler, Danielle L
- Spahr, Henrik
- Schöndorf, Thomas
- Shearwood, Ann-Marie J
- Viola, Helena M
- Siira, Stefan J
- Hool, Livia C
- Milenkovic, Dusanka
- Larsson, Nils-Göran
- Rackham, Oliver
- Filipovska, Aleksandra
Producer: 20190903
In:
Cell reports vol. 23
Availability: No items available.
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12.
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Stress signaling and cellular proliferation reverse the effects of mitochondrial mistranslation. [electronic resource] by
- Ferreira, Nicola
- Perks, Kara L
- Rossetti, Giulia
- Rudler, Danielle L
- Hughes, Laetitia A
- Ermer, Judith A
- Scott, Louis H
- Kuznetsova, Irina
- Richman, Tara R
- Narayana, Vinod K
- Abudulai, Laila N
- Shearwood, Anne-Marie J
- Cserne Szappanos, Henrietta
- Tull, Dedreia
- Yeoh, George C
- Hool, Livia C
- Filipovska, Aleksandra
- Rackham, Oliver
Producer: 20200320
In:
The EMBO journal vol. 38
Availability: No items available.
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