In vivo evidence of mitochondrial dysfunction and altered redox homeostasis in a genetic mouse model of propionic acidemia: Implications for the pathophysiology of this disorder. [electronic resource]
Producer: 20180109Description: 1-12 p. digitalISSN:- 1873-4596
- Animals
- Antioxidants -- metabolism
- DNA, Mitochondrial -- genetics
- Disease Models, Animal
- Homeostasis
- Humans
- Hydrogen Peroxide -- metabolism
- Lipid Peroxidation -- genetics
- Methylmalonyl-CoA Decarboxylase -- genetics
- Mice
- Mitochondria -- genetics
- Oxidation-Reduction
- Oxidative Stress -- genetics
- Propionic Acidemia -- genetics
- Protein Array Analysis
- Reactive Oxygen Species -- metabolism
- Superoxides -- metabolism
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Publication Type: Journal Article
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