Pharmacological Interventions to Ameliorate Neuropathological Symptoms in a Mouse Model of Lafora Disease. [electronic resource]
Producer: 20161213Description: 1296-1309 p. digitalISSN:- 1559-1182
- Animals
- Brain -- pathology
- Disease Models, Animal
- Fluorescent Antibody Technique
- Gliosis -- complications
- Glucans -- metabolism
- Hippocampus -- drug effects
- Inclusion Bodies -- drug effects
- Lafora Disease -- drug therapy
- Metformin -- pharmacology
- Mice, Inbred C57BL
- Mice, Knockout
- Nerve Degeneration -- complications
- Neuropsychological Tests
- Phenylbutyrates -- pharmacology
- Protein Aggregates -- drug effects
- Trehalose -- pharmacology
- Ubiquitin-Protein Ligases -- deficiency
- Ubiquitinated Proteins -- metabolism
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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