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Structural basis of pharmacological chaperoning for human β-galactosidase. [electronic resource] by
- Suzuki, Hironori
- Ohto, Umeharu
- Higaki, Katsumi
- Mena-Barragán, Teresa
- Aguilar-Moncayo, Matilde
- Ortiz Mellet, Carmen
- Nanba, Eiji
- Garcia Fernandez, Jose M
- Suzuki, Yoshiyuki
- Shimizu, Toshiyuki
Producer: 20141028
In:
The Journal of biological chemistry vol. 289
Availability: No items available.
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10.
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Cyclodextrin-mediated crystallization of acid β-glucosidase in complex with amphiphilic bicyclic nojirimycin analogues. [electronic resource] by
- Brumshtein, Boris
- Aguilar-Moncayo, Matilde
- Benito, Juan M
- García Fernandez, José M
- Silman, Israel
- Shaaltiel, Yoseph
- Aviezer, David
- Sussman, Joel L
- Futerman, Anthony H
- Ortiz Mellet, Carmen
Producer: 20110909
In:
Organic & biomolecular chemistry vol. 9
Availability: No items available.
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11.
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6-Amino-6-deoxy-5,6-di-N-(N'-octyliminomethylidene)nojirimycin: synthesis, biological evaluation, and crystal structure in complex with acid beta-glucosidase. [electronic resource] by
- Brumshtein, Boris
- Aguilar-Moncayo, Matilde
- García-Moreno, M Isabel
- Ortiz Mellet, Carmen
- García Fernández, José M
- Silman, Israel
- Shaaltiel, Yoseph
- Aviezer, David
- Sussman, Joel L
- Futerman, Anthony H
Producer: 20090930
In:
Chembiochem : a European journal of chemical biology vol. 10
Availability: No items available.
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12.
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A Fluorescent sp2-iminosugar with pharmacological chaperone activity for gaucher disease: synthesis and intracellular distribution studies. [electronic resource] by
- Luan, Zhuo
- Higaki, Katsumi
- Aguilar-Moncayo, Matilde
- Li, Linjing
- Ninomiya, Haruaki
- Nanba, Eiji
- Ohno, Kousaku
- García-Moreno, M Isabel
- Ortiz Mellet, Carmen
- García Fernández, José M
- Suzuki, Yoshiyuki
Producer: 20110503
In:
Chembiochem : a European journal of chemical biology vol. 11
Availability: No items available.
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13.
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A bicyclic 1-deoxygalactonojirimycin derivative as a novel pharmacological chaperone for GM1 gangliosidosis. [electronic resource] by
- Takai, Tomoko
- Higaki, Katsumi
- Aguilar-Moncayo, Matilde
- Mena-Barragán, Teresa
- Hirano, Yuki
- Yura, Kei
- Yu, Liang
- Ninomiya, Haruaki
- García-Moreno, M Isabel
- Sakakibara, Yasubumi
- Ohno, Kousaku
- Nanba, Eiji
- Ortiz Mellet, Carmen
- García Fernández, José M
- Suzuki, Yoshiyuki
Producer: 20131022
In:
Molecular therapy : the journal of the American Society of Gene Therapy vol. 21
Availability: No items available.
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14.
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Scalable syntheses of both enantiomers of DNJNAc and DGJNAc from glucuronolactone: the effect of N-alkylation on hexosaminidase inhibition. [electronic resource] by
- Glawar, Andreas F G
- Best, Daniel
- Ayers, Benjamin J
- Miyauchi, Saori
- Nakagawa, Shinpei
- Aguilar-Moncayo, Matilde
- García Fernández, José M
- Ortiz Mellet, Carmen
- Crabtree, Elizabeth V
- Butters, Terry D
- Wilson, Francis X
- Kato, Atsushi
- Fleet, George W J
Producer: 20121130
In:
Chemistry (Weinheim an der Bergstrasse, Germany) vol. 18
Availability: No items available.
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