Your search returned 408 results.

Results
	241.	Gerstmann-Sträussler-Scheinker: a new phenotype with 'curly' PrP deposits. [electronic resource] by Colucci, Monica Moleres, Francisco J Xie, Zhi-Liang Ray-Chaudhury, Abhik Gutti, Sujata Butefisch, Cathrin M Cervenakova, Larisa Wang, Wen Goldfarb, Lev G Kong, Qingzhong Ghetti, Bernardino Chen, Shu G Gambetti, Pierluigi Producer: 20060829 In: Journal of neuropathology and experimental neurology vol. 65 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	242.	Substitutions at residue 211 in the prion protein drive a switch between CJD and GSS syndrome, a new mechanism governing inherited neurodegenerative disorders. [electronic resource] by Peoc'h, Katell Levavasseur, Etienne Delmont, Emilien De Simone, Alfonso Laffont-Proust, Isabelle Privat, Nicolas Chebaro, Yassmine Chapuis, Céline Bedoucha, Pierre Brandel, Jean-Philippe Laquerriere, Annie Kemeny, Jean-Louis Hauw, Jean-Jacques Borg, Michel Rezaei, Human Derreumaux, Philippe Laplanche, Jean-Louis Haïk, Stéphane Producer: 20130515 In: Human molecular genetics vol. 21 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	243.	Transmission of human spongiform encephalopathies to experimental animals: comparison of the chimpanzee and squirrel monkey. [electronic resource] by Asher, D M Gibbs, C J Sulima, M P Bacote, A Amyx, H Gajdusek, D C Producer: 19940203 In: Developments in biological standardization vol. 80 Availability: No items available. Save to lists Add to cart (remove)
	244.	Prominent psychiatric features and early onset in an inherited prion disease with a new insertional mutation in the prion protein gene. [electronic resource] by Laplanche, J L Hachimi, K H Durieux, I Thuillet, P Defebvre, L Delasnerie-Lauprêtre, N Peoc'h, K Foncin, J F Destée, A Producer: 20000120 In: Brain : a journal of neurology vol. 122 ( Pt 12) Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	245.	Very long term studies of the seeding of beta-amyloidosis in primates. [electronic resource] by Ridley, R M Baker, H F Windle, C P Cummings, R M Producer: 20070502 In: Journal of neural transmission (Vienna, Austria : 1996) vol. 113 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	246.	Rapamycin delays disease onset and prevents PrP plaque deposition in a mouse model of Gerstmann-Sträussler-Scheinker disease. [electronic resource] by Cortes, Constanza J Qin, Kefeng Cook, Julie Solanki, Ani Mastrianni, James A Producer: 20121116 In: The Journal of neuroscience : the official journal of the Society for Neuroscience vol. 32 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	247.	A case of sporadic Creutzfeldt-Jakob disease with a Gerstmann-Sträussler-Scheinker phenotype but no alterations in the PRNP gene. [electronic resource] by Liberski, P P Barcikowska, M Cervenakova, L Bratosiewicz, J Marczewska, M Brown, P Gajdusek, D C Producer: 19990108 In: Acta neuropathologica vol. 96 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	248.	Prion diseases. [electronic resource] by Knight, R S G Will, R G Producer: 20040326 In: Journal of neurology, neurosurgery, and psychiatry vol. 75 Suppl 1 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	249.	Gerstmann-Sträussler-Scheinker disease with P102L-V129 mutation: a case with psychiatric manifestations at onset. [electronic resource] by Bianca, Marco Bianca, Sebastiano Vecchio, Ignazio Raffaele, Rocco Ingegnosi, Carmela Nicoletti, Francesco Producer: 20040629 In: Annales de genetique vol. 46 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	250.	[Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies. Part I]. [electronic resource] by Zaborowski, Adam Producer: 20040917 In: Psychiatria polska vol. 38 Availability: No items available. Save to lists Add to cart (remove)
	251.	Colocalization of prion protein and beta protein in the same amyloid plaques in patients with Gerstmann-Sträussler syndrome. [electronic resource] by Miyazono, M Kitamoto, T Iwaki, T Tateishi, J Producer: 19920529 In: Acta neuropathologica vol. 83 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	252.	The prion diseases. [electronic resource] by Mastrianni, J A Roos, R P Producer: 20010215 In: Seminars in neurology vol. 20 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	253.	A novel seven-octapeptide repeat insertion in the prion protein gene (PRNP) in a Dutch pedigree with Gerstmann-Sträussler-Scheinker disease phenotype: comparison with similar cases from the literature. [electronic resource] by Jansen, Casper Voet, Willem Head, Mark W Parchi, Piero Yull, Helen Verrips, Aad Wesseling, Pieter Meulstee, Jan Baas, Frank van Gool, Willem A Ironside, James W Rozemuller, Annemieke J M Producer: 20111114 In: Acta neuropathologica vol. 121 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	254.	Prion protein amyloidosis with divergent phenotype associated with two novel nonsense mutations in PRNP. [electronic resource] by Jansen, Casper Parchi, Piero Capellari, Sabina Vermeij, Ad J Corrado, Patrizia Baas, Frank Strammiello, Rosaria van Gool, Willem A van Swieten, John C Rozemuller, Annemieke J M Producer: 20100302 In: Acta neuropathologica vol. 119 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	255.	Spontaneous neurodegeneration in transgenic mice with prion protein codon 101 proline----leucine substitution. [electronic resource] by Hsiao, K Scott, M Foster, D DeArmond, S J Groth, D Serban, H Prusiner, S B Producer: 19920228 In: Annals of the New York Academy of Sciences vol. 640 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	256.	Proteinase-K-resistant prion protein isoforms in Gerstmann-Sträussler-Scheinker disease (Indiana kindred). [electronic resource] by Piccardo, P Seiler, C Dlouhy, S R Young, K Farlow, M R Prelli, F Frangione, B Bugiani, O Tagliavini, F Ghetti, B Producer: 19970107 In: Journal of neuropathology and experimental neurology vol. 55 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	257.	Prion protein with Y145STOP mutation induces mitochondria-mediated apoptosis and PrP-containing deposits in vitro. [electronic resource] by Hachiya, Naomi S Watanabe, Kota Kawabata, Makiko Y Jozuka, Akiko Kozuka, Yoshimichi Sakasegawa, Yuji Kaneko, Kiyotoshi Producer: 20050413 In: Biochemical and biophysical research communications vol. 327 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	258.	A68 is a component of paired helical filaments of Gerstmann-Sträussler-Scheinker disease, Indiana kindred. [electronic resource] by Tagliavini, F Giaccone, G Prelli, F Verga, L Porro, M Trojanowski, J Q Farlow, M R Frangione, B Ghetti, B Bugiani, O Producer: 19930930 In: Brain research vol. 616 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	259.	A comparative study of abnormal prion protein isoforms between Gerstmann-Sträussler-Scheinker syndrome and Creutzfeldt-Jakob disease. [electronic resource] by Furukawa, H Doh-ura, K Kikuchi, H Tateishi, J Iwaki, T Producer: 19981015 In: Journal of the neurological sciences vol. 158 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)
	260.	A novel Gerstmann-Sträussler-Scheinker disease mutation defines a precursor for amyloidogenic 8 kDa PrP fragments and reveals N-terminal structural changes shared by other GSS alleles. [electronic resource] by Mercer, Robert C C Daude, Nathalie Dorosh, Lyudmyla Fu, Ze-Lin Mays, Charles E Gapeshina, Hristina Wohlgemuth, Serene L Acevedo-Morantes, Claudia Y Yang, Jing Cashman, Neil R Coulthart, Michael B Pearson, Dawn M Joseph, Jeffrey T Wille, Holger Safar, Jiri G Jansen, Gerard H Stepanova, Maria Sykes, Brian D Westaway, David Producer: 20180706 In: PLoS pathogens vol. 14 Online resources: Available from publisher's website Availability: No items available. Save to lists Add to cart (remove)

First
Previous
4
5
6
7
8
9
10
11
12
13
14
15
16
17
18
19
20
21
Next
Last

Refine your search

Availability

Authors

Topics

Languages

Your search returned 408 results.