Tabrizi, S J

Biochemical abnormalities and excitotoxicity in Huntington's disease brain. [electronic resource] - Annals of neurology Jan 1999 - 25-32 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0364-5134

10.1002/1531-8249(199901)45:1<25::aid-art6>3.0.co;2-e doi


Aconitate Hydratase--metabolism
Adult
Aged
Aged, 80 and over
Brain Chemistry
Brain Diseases--metabolism
Electron Transport--physiology
Electron Transport Complex II
Electron Transport Complex III--metabolism
Enzyme Activation--drug effects
Female
Fibroblasts
Glutathione--analogs & derivatives
Humans
Huntingtin Protein
Huntington Disease--metabolism
Male
Middle Aged
Mitochondria--drug effects
Multienzyme Complexes--metabolism
Nerve Tissue Proteins--genetics
Neuroblastoma
Neuroprotective Agents--pharmacology
Neurotoxins--metabolism
Nitric Oxide--metabolism
Nitroso Compounds--pharmacology
Nuclear Proteins--genetics
Oxidoreductases--metabolism
S-Nitrosoglutathione
Succinate Cytochrome c Oxidoreductase--metabolism
Succinate Dehydrogenase--metabolism
Trinucleotide Repeats
Tumor Cells, Cultured--enzymology