Feillet, F
Alternative pathway therapy for urea cycle disorders. [electronic resource]
- Journal of inherited metabolic disease 1998
- 101-11 p. digital
Publication Type: Journal Article; Review
0141-8955
10.1023/a:1005365825875 doi
Amino Acid Metabolism, Inborn Errors--diet therapy
Animals
Arginine--metabolism
Benzoates--adverse effects
Benzoic Acid
Child
Citrulline--metabolism
Combined Modality Therapy
Female
Humans
Male
Nitrogen--metabolism
Phenylacetates--therapeutic use
Phenylbutyrates--adverse effects
Urea--metabolism