TY - GEN AU - Hegde,R S AU - Mastrianni,J A AU - Scott,M R AU - DeFea,K A AU - Tremblay,P AU - Torchia,M AU - DeArmond,S J AU - Prusiner,S B AU - Lingappa,V R TI - A transmembrane form of the prion protein in neurodegenerative disease SN - 0036-8075 PY - 1998///0223 KW - Amino Acid Sequence KW - Animals KW - Brain KW - metabolism KW - Cricetinae KW - Endopeptidases KW - Endoplasmic Reticulum KW - chemistry KW - Gerstmann-Straussler-Scheinker Disease KW - Humans KW - Intracellular Membranes KW - Mesocricetus KW - Mice KW - Mice, Transgenic KW - Molecular Sequence Data KW - Mutation KW - Neurodegenerative Diseases KW - etiology KW - PrPC Proteins KW - biosynthesis KW - PrPSc Proteins KW - Prion Diseases KW - Prions KW - Protein Conformation N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S UR - https://doi.org/10.1126/science.279.5352.827 ER -