TY - GEN AU - Furlan,M AU - Robles,R AU - Solenthaler,M AU - Wassmer,M AU - Sandoz,P AU - Lämmle,B TI - Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura SN - 0006-4971 PY - 1997///0603 KW - ADAM Proteins KW - ADAMTS13 Protein KW - Adult KW - Anemia, Hemolytic KW - blood KW - Disulfides KW - Female KW - Humans KW - Macromolecular Substances KW - Male KW - Metalloendopeptidases KW - Middle Aged KW - Nuclear Family KW - Protease Inhibitors KW - pharmacology KW - Purpura, Thrombotic Thrombocytopenic KW - Reference Values KW - von Willebrand Factor KW - metabolism N1 - Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't ER -