TY - GEN AU - Kuznetsov,A V AU - Winkler,K AU - Kirches,E AU - Lins,H AU - Feistner,H AU - Kunz,W S TI - Application of inhibitor titrations for the detection of oxidative phosphorylation defects in saponin-skinned muscle fibers of patients with mitochondrial diseases SN - 0006-3002 PY - 1997///0519 KW - Adult KW - Azides KW - pharmacology KW - Biopsy KW - Electron Transport Complex I KW - Enzyme Inhibitors KW - Female KW - Humans KW - In Vitro Techniques KW - Male KW - Mitochondrial Myopathies KW - diagnosis KW - NADH, NADPH Oxidoreductases KW - metabolism KW - Oligomycins KW - Oxidative Phosphorylation KW - drug effects KW - Oxygen Consumption KW - Proton-Translocating ATPases KW - antagonists & inhibitors KW - Rotenone N1 - Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1016/s0925-4439(96)00072-5 ER -