Kuznetsov, A V

Application of inhibitor titrations for the detection of oxidative phosphorylation defects in saponin-skinned muscle fibers of patients with mitochondrial diseases. [electronic resource] - Biochimica et biophysica acta Apr 1997 - 142-50 p. digital

Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't

0006-3002

10.1016/s0925-4439(96)00072-5 doi


Adult
Azides--pharmacology
Biopsy
Electron Transport Complex I
Enzyme Inhibitors--pharmacology
Female
Humans
In Vitro Techniques
Male
Mitochondrial Myopathies--diagnosis
NADH, NADPH Oxidoreductases--metabolism
Oligomycins--pharmacology
Oxidative Phosphorylation--drug effects
Oxygen Consumption--drug effects
Proton-Translocating ATPases--antagonists & inhibitors
Rotenone--pharmacology