Application of inhibitor titrations for the detection of oxidative phosphorylation defects in saponin-skinned muscle fibers of patients with mitochondrial diseases. [electronic resource]
- Biochimica et biophysica acta Apr 1997
- 142-50 p. digital
Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't
0006-3002
10.1016/s0925-4439(96)00072-5 doi
Adult Azides--pharmacology Biopsy Electron Transport Complex I Enzyme Inhibitors--pharmacology Female Humans In Vitro Techniques Male Mitochondrial Myopathies--diagnosis NADH, NADPH Oxidoreductases--metabolism Oligomycins--pharmacology Oxidative Phosphorylation--drug effects Oxygen Consumption--drug effects Proton-Translocating ATPases--antagonists & inhibitors Rotenone--pharmacology