TY - GEN AU - Fries,M H AU - Rinaldo,P AU - Schmidt-Sommerfeld,E AU - Jurecki,E AU - Packman,S TI - Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy SN - 0022-3476 PY - 1996///1022 KW - Amino Acid Metabolism, Inborn Errors KW - drug therapy KW - Carnitine KW - administration & dosage KW - Child KW - Female KW - Glycine KW - Hemiterpenes KW - Humans KW - Isovaleryl-CoA Dehydrogenase KW - Leucine KW - metabolism KW - Oxidoreductases KW - Oxidoreductases Acting on CH-CH Group Donors KW - Pentanoic Acids KW - blood N1 - Publication Type: Journal Article UR - https://doi.org/10.1016/s0022-3476(96)70081-1 ER -