Fries, M H <br/><br/>
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.  [electronic resource] 

 -  The Journal of pediatrics  Sep 1996 
 - 449-52 p.  digital 
<br/><br/> Publication Type: Journal Article 
<br/><br/><label>ISSN: </label>0022-3476 
<br/><br/><label>Standard No.: </label>10.1016/s0022-3476(96)70081-1  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Amino Acid Metabolism, Inborn Errors--drug therapy<br/>Carnitine--administration & dosage<br/>Child<br/>Female<br/>Glycine--administration & dosage<br/>Hemiterpenes<br/>Humans<br/>Isovaleryl-CoA Dehydrogenase<br/>Leucine--metabolism<br/>Oxidoreductases--metabolism<br/>Oxidoreductases Acting on CH-CH Group Donors<br/>Pentanoic Acids--blood