TY - GEN AU - Kondo,K H AU - Maeda,Y AU - Setoguchi,T TI - [Congenital disorders of the bile acid metabolism (3 beta-hydroxy-delta 5-steroid dehydrogenase/isomerase deficiency, delta 4-3-oxosteroid 5 beta-reductase deficiency, cerebrotendinous xanthomatosis, and peroxisomal disorders] PY - 1996///0318 KW - Bile Acids and Salts KW - metabolism KW - Brain Diseases KW - Humans KW - Multienzyme Complexes KW - deficiency KW - Oxidoreductases KW - Peroxisomal Disorders KW - Progesterone Reductase KW - Steroid Isomerases KW - Tendons KW - Xanthomatosis N1 - Publication Type: Journal Article; Review ER -