Määttä, A

Fibroblast expression of collagens and proteoglycans is altered in aspartylglucosaminuria, a lysosomal storage disease. [electronic resource] - Biochimica et biophysica acta Feb 1994 - 264-70 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0006-3002

10.1016/0925-4439(94)90005-1 doi


Acetylglucosamine--analogs & derivatives
Aspartylglucosaminuria
Cells, Cultured
Collagen--metabolism
Extracellular Matrix--metabolism
Fibroblasts--metabolism
Humans
Lysosomal Storage Diseases--metabolism
Procollagen--genetics
Proteoglycans--metabolism
RNA, Messenger--analysis
Skin--metabolism
Sulfur Radioisotopes