Lamhonwah, A M

Correction of the metabolic defect in propionic acidemia fibroblasts by microinjection of a full-length cDNA or RNA transcript encoding the propionyl-CoA carboxylase beta subunit. [electronic resource] - Genomics Feb 1994 - 500-5 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0888-7543

10.1006/geno.1994.1099 doi


Amino Acid Sequence
Base Sequence
Carboxy-Lyases--biosynthesis
Cell Nucleus
Cells, Cultured
Clone Cells--metabolism
Cytoplasm
DNA, Complementary--genetics
Fibroblasts--enzymology
Genetic Vectors
Humans
Metabolism, Inborn Errors--genetics
Methylmalonyl-CoA Decarboxylase
Microinjections
Mitochondria--enzymology
Molecular Sequence Data
Propionates--blood
RNA, Messenger--genetics
Recombinant Fusion Proteins--biosynthesis