Williams, J C <br/><br/>
Defective catabolism of low-density lipoprotein by fibroblasts from patients with I-cell disease.  [electronic resource] 

 -  The Biochemical journal  Jan 1982 
 - 183-90 p.  digital 
<br/><br/> Publication Type: Comparative Study; Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S. 
<br/><br/><label>ISSN: </label>0264-6021 
<br/><br/><label>Standard No.: </label>10.1042/bj2020183  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Cells, Cultured<br/>Fibroblasts--drug effects<br/>Humans<br/>Hydroxymethylglutaryl CoA Reductases--metabolism<br/>Hyperlipoproteinemia Type II--metabolism<br/>Infant<br/>Ketocholesterols--pharmacology<br/>Lipoproteins, LDL--metabolism<br/>Mucolipidoses--metabolism<br/>Protein Binding<br/>Skin--metabolism