Trijbels, J M

Biochemical studies in the liver and muscle of patients with Zellweger syndrome. [electronic resource] - Pediatric research Jun 1983 - 514-7 p. digital

Publication Type: Journal Article

0031-3998

10.1203/00006450-198306000-00018 doi


Brain Diseases--metabolism
Child, Preschool
Electron Transport
Humans
Infant
Kidney Diseases--metabolism
Liver Diseases--metabolism
Metabolism, Inborn Errors--metabolism
Microbodies--metabolism
Mitochondria, Liver--analysis
Mitochondria, Muscle--analysis
Oxygen Consumption
Pipecolic Acids--metabolism
Syndrome