TY - GEN AU - Spellacy,E AU - Shull,R M AU - Constantopoulos,G AU - Neufeld,E F TI - A canine model of human alpha-L-iduronidase deficiency SN - 0027-8424 PY - 1983///1028 KW - Animals KW - Cells, Cultured KW - Disease Models, Animal KW - Dog Diseases KW - enzymology KW - Dogs KW - Female KW - Fibroblasts KW - Glycoside Hydrolases KW - deficiency KW - Humans KW - Iduronidase KW - Leukocytes KW - Lysosomes KW - Male KW - Mucopolysaccharidosis I KW - Pedigree KW - Skin N1 - Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S UR - https://doi.org/10.1073/pnas.80.19.6091 ER -