Brandt, I K

Propionicacidemia (ketotic hyperglycinemia): dietary treatment resulting in normal growth and development. [electronic resource] - Pediatrics Mar 1974 - 391-5 p. digital

Publication Type: Journal Article

0031-4005


Acidosis--therapy
Amino Acid Metabolism, Inborn Errors--enzymology
Body Height
Body Weight
Carboxy-Lyases--metabolism
Child
Coenzyme A
Diet Therapy
Dietary Carbohydrates--administration & dosage
Dietary Proteins--adverse effects
Female
Follow-Up Studies
Glycine--metabolism
Humans
Intelligence
Ketone Bodies--metabolism
Propionates--metabolism