Kappas, A Studies in porphyria. I. A defect in the reductive transformation of natural steroid hormones in the hereditary liver disease, acute intermittent porphyria. [electronic resource] - The Journal of experimental medicine Nov 1972 - 1043-53 p. digital Publication Type: Journal Article ISSN: 0022-1007 Standard No.: 10.1084/jem.136.5.1043 doi Subjects--Topical Terms: 5-Aminolevulinate Synthetase--metabolismAdultAndrosterone--metabolismCarbon IsotopesDehydroepiandrosterone--metabolismEnzyme InductionEtiocholanolone--metabolismFemaleHumansLiver--enzymologyLiver Diseases--enzymologyMaleMiddle AgedPorphyrias--enzymologyTestosterone--metabolism