Kappas, A

Studies in porphyria. I. A defect in the reductive transformation of natural steroid hormones in the hereditary liver disease, acute intermittent porphyria. [electronic resource] - The Journal of experimental medicine Nov 1972 - 1043-53 p. digital

Publication Type: Journal Article

0022-1007

10.1084/jem.136.5.1043 doi


5-Aminolevulinate Synthetase--metabolism
Adult
Androsterone--metabolism
Carbon Isotopes
Dehydroepiandrosterone--metabolism
Enzyme Induction
Etiocholanolone--metabolism
Female
Humans
Liver--enzymology
Liver Diseases--enzymology
Male
Middle Aged
Porphyrias--enzymology
Testosterone--metabolism