TY - GEN AU - O'Brien,J F AU - Cantz,M AU - Spranger,J TI - Maroteaux-Lamy disease (mucopolysaccharidosis VI), subtype A: deficiency of a N-acetylgalactosamine-4-sulfatase SN - 0006-291X PY - 1975///0125 KW - Carbon Radioisotopes KW - Cell Line KW - Chondroitin KW - Chromatography, Ion Exchange KW - Chromatography, Paper KW - Dermatan Sulfate KW - metabolism KW - Electrophoresis KW - Fibroblasts KW - Galactosamine KW - analogs & derivatives KW - Glucosamine KW - Humans KW - Lyases KW - Molecular Conformation KW - Mucopolysaccharidoses KW - enzymology KW - Sulfatases KW - deficiency KW - Sulfur Radioisotopes KW - Sulfuric Acids N1 - Publication Type: Journal Article UR - https://doi.org/10.1016/0006-291x(74)90435-5 ER -