Saudubray, J M [Lactic acidosis, hypoglycemia and hepatomegaly due to hereditary defect in hepatic fructose-1, 6-diphosphatase]. [electronic resource] - Archives francaises de pediatrie - 609-32 p. digital Publication Type: English Abstract; Journal Article ISSN: 0003-9764 Subjects--Topical Terms: Acid-Base EquilibriumAcidosis--etiologyCarbohydrate Metabolism, Inborn Errors--complicationsChildChild, PreschoolFastingFatty Liver--etiologyFemaleFructoseFructose-Bisphosphatase--metabolismGlucagonGlucose Tolerance TestGlycolysisHepatomegaly--etiologyHumansHypoglycemia--etiologyLactates--bloodMaleNAD--metabolismNADP--metabolism