Saudubray, J M

[Lactic acidosis, hypoglycemia and hepatomegaly due to hereditary defect in hepatic fructose-1, 6-diphosphatase]. [electronic resource] - Archives francaises de pediatrie - 609-32 p. digital

Publication Type: English Abstract; Journal Article

0003-9764


Acid-Base Equilibrium
Acidosis--etiology
Carbohydrate Metabolism, Inborn Errors--complications
Child
Child, Preschool
Fasting
Fatty Liver--etiology
Female
Fructose
Fructose-Bisphosphatase--metabolism
Glucagon
Glucose Tolerance Test
Glycolysis
Hepatomegaly--etiology
Humans
Hypoglycemia--etiology
Lactates--blood
Male
NAD--metabolism
NADP--metabolism